Jove
Visualize
Contact Us
  1. Home
  2. Research Domains
  3. Biomedical And Clinical Sciences
  4. Neurosciences
  5. Sensory Systems
  6. Development And Validation Of An Lc-ms/ms Assay For Quantitative Analysis Of Nusinersen In Human Csf And Plasma

Development and Validation of an LC-MS/MS Assay for Quantitative Analysis of Nusinersen in Human CSF and Plasma

Tingting Xu1,2, Wei Zuo1,2, Zhuo Sun1,2

  • 1Department of Pharmacy, Peking Union Medical College Hospital, Chinese Academy of Medical Sciences and Peking Union Medical College, Beijing, China.

Biomedical Chromatography : BMC|June 14, 2025

Related Experiment Videos

View abstract on PubMed

Summary

A new method accurately measures nusinersen drug levels in spinal muscular atrophy (SMA) patients

Area of Science:

  • Pharmacology
  • Analytical Chemistry
  • Biochemistry

Background:

  • Nusinersen is a key treatment for spinal muscular atrophy (SMA).
  • Pharmacokinetic data for nusinersen in Chinese SMA patients is currently unavailable.
  • Accurate quantification methods are essential for therapeutic drug monitoring.

Purpose of the Study:

  • To develop and validate a sensitive LC-MS/MS method for nusinersen quantification.
  • To enable pharmacokinetic studies in Chinese SMA patient populations.
  • To establish a reliable analytical tool for therapeutic drug monitoring.

Main Methods:

  • Protein precipitation for sample preparation.
  • Reversed-phase liquid chromatography (LC) using a C18 column.
  • Tandem mass spectrometry (MS/MS) detection in negative ion MRM mode.

Main Results:

  • The LC-MS/MS method was successfully validated for human plasma and cerebrospinal fluid (CSF).
  • Quantification ranges were established: 5.00–1000 ng/mL for plasma and 2.00–400 ng/mL for CSF.
  • This is the first reported LC-MS/MS quantification of nusinersen in human plasma and CSF.

Conclusions:

  • A reliable and validated LC-MS/MS method for nusinersen quantification has been developed.
  • This methodology will facilitate crucial pharmacokinetic studies in Chinese SMA patients.
  • The method supports the clinical application of nusinersen in this population.
Keywords:
IP‐RP‐LC/MS/MSantisense oligonucleotidenusinersenspinal muscular atrophy

Related Experiment Videos

Related Concept Videos

JoVE
x logofacebook logolinkedin logoyoutube logo
ABOUT JoVE
OverviewLeadershipBlogJoVE Help Center
AUTHORS
Publishing ProcessEditorial BoardScope & PoliciesPeer ReviewFAQSubmit
LIBRARIANS
TestimonialsSubscriptionsAccessResourcesLibrary Advisory BoardFAQ
RESEARCH
JoVE JournalMethods CollectionsJoVE Encyclopedia of ExperimentsArchive
EDUCATION
JoVE CoreJoVE BusinessJoVE Science EducationJoVE Lab ManualFaculty Resource CenterFaculty Site

Terms & Conditions of Use
Privacy Policy
Policies